Overall, 9/36 pts (5 DCM, 3 MPCM, 1 mastocytoma) presented spontaneous complete regression of cutaneous lesions after a median time of 25 months (range 17 months-25 years).<h4>Conclusion</h4>c-<i>KIT</i> mutations resulted in 35% of the children tested. The gene discussed is KIT; the disease is mastocytoma.