To obtain an updated overview of thoracic presentations, we performed a PubMed search spanning 2002-2025 using the terms “SMARCB1/INI1-deficient thoracic tumors”, “SMARCB1/INI1-deficient lung carcinoma”, and “SMARCB1/INI1-deficient lung cancer”, identifying 15 cases in the literature (including the present one), as summarized in Table 2. This evidence concerns the gene SMARCB1 and neoplasm of thorax.