Pulmonary alveolar microlithiasis (PAM) is a fascinating, rare lung disease, first described in 1686 and later named as Pulmonary Alveolar Microlithiasis in 1933 by Puhr [4].It is an autosomal recessive condition; mutations in the SLC34A2 gene have been identified as the culprit in familial cases [4,5]. Here, SLC34A2 is linked to pulmonary alveolar microlithiasis.