Allgrove syndrome (AS), also known as “3 A” syndrome, is a rare autosomal recessive disorder that was first described by Allgrove and his colleagues in 1978.[1] It constitutes one of the rare genetic diseases affecting approximately 1 in a million people in the general population, although this estimate might be lower than the actual rate due to underdiagnosis.[2] The condition arises due to alterations in the AAAS gene located on chromosome 12q13. This evidence concerns the gene AAAS and Triple A syndrome.