DSPP and osteogenesis imperfecta: Varying degrees of wear leads to enamel loss and the exposed underlying amber-colored dentin; (2) Radiographic imaging reveals obliterated pulp chambers, root canals and cervical constriction; (3) The patients typically do not show signs of osteogenesis imperfecta, although a few may exhibit sensorineural hearing loss; (4) Patients often present with a family history of an autosomal dominant inheritance pattern; (5) Auxiliary genetic testing often identifies mutations in dentin sialophosphoprotein (DSPP) gene.6,84