Our main differential morphological diagnoses included CIC‐rearranged sarcoma, primary intracranial sarcoma (DICER1‐mutant), diffuse midline glioma, diffuse pediatric‐type high‐grade glioma, sarcomas, and plasmacytic‐rich meningioma, as the sarcomatoid morphology suggested a glial origin. Here, DICER1 is linked to diffuse midline glioma.