It shares morphological, molecular, and clinical features with other SMARCA4-deficient neoplasms, such as SMARCA4-deficient thoracic sarcoma and small cell carcinoma of the ovary, hypercalcemic type (SCCOHT), suggesting a spectrum of related tumors linked to SWI/SNF complex dysfunction [77,78,121,122,123]. The gene discussed is SMARCA4; the disease is neoplasm.