SLC27A4 and ichthyosis prematurity syndrome: IPS is caused by variants of the SLC2A4 gene encoding the fatty acid transporter protein 4 (FATP4) [5] and is inherited in an autosomal recessive manner. Although IPS has a favorable prognosis, neonatal complications can be fatal without implementing respiratory support in cases of respiratory distress, and recognizing this entity is thus vital for appropriate and planned management.