Inherited predispositions to meningiomas, such as neurofibromatosis type 2, nevoid basal cell carcinoma syndrome, multiple endocrine neoplasia 1 (MEN1), Cowden syndrome, Werner syndrome, BAP1 tumor predisposition syndrome, Rubinstein-Taybi syndrome, and familial meningiomatosis caused by germline variants in the SMARCB1 and SMARCE1 genes, may impact the incidence of subsequent meningiomas, multiple meningiomas, and potentially the prognosis among childhood cancer survivors.39 Furthermore, biologic descriptions of the subsequent meningioma cases were limited to histologic coding. The gene discussed is SMARCE1; the disease is BAP1-related tumor predisposition syndrome.