Stargardt disease 4 (STGD4) shares clinical and pathological features with ABCA4-related Stargardt disease type 1 (STGD1) and the atrophic form of AMD, including central photoreceptor degeneration and RPE atrophy [19,20,21]. The gene discussed is ABCA4; the disease is severe early-childhood-onset retinal dystrophy.