Interestingly, none of our cases showed associated visceral lesions typical of VHL, possibly due to the relatively young age of the patients, as the mean ages of onset for VHL associated renal cell carcinomas, pheocromocytomas or pancreatic tumors are 37, 30, and 36, respectively, with a large range of approximately ±30 years [8]. Here, VHL is linked to renal cell carcinoma.