Alternatively, the WT1 NM_024426.6:c.1432+1G>A likely pathogenic splice (KST) variant was identified in a FSGS patient who also presented with Frasier syndrome, and in another patient with monogenic FSGS who achieved transient partial remission when started on cyclosporin A (CsA) therapy, a second-line calcineurin inhibitor [22]. This evidence concerns the gene WT1 and Frasier syndrome.