Fragile X-Associated Tremor/Ataxia Syndrome (FXTAS) is an adult-onset neurodegenerative disorder that affects ~10 – 60% of carriers of the X-linked FMR1 premutation, a repetitive CGG sequence (~55 – 200 repeats in length) [1–3]. Here, FMR1 is linked to fragile X-associated tremor/ataxia syndrome.