Severe albuminuria (A3, i.e., > 30 g/mol) was observed in 4 of 6 cases (66%) with PAX2 LOF variants and available data, that is, in 3 kidney transplantation patients and in 1 patient with CKD stage G3 at the age of 8 years (Table 2 and Figure 3c). Here, PAX2 is linked to chronic kidney disease.