Other IMD resulting in hyperuricemia are related to UA overproduction due to nucleotide depletion (increased ATP consumption or impaired ATP regeneration) and include the following: (i) hereditary fructose intolerance; (ii) fructose-1,6-biphosphatase deficiency; (iii) GSD types III, V, and VII; (iv) MCAD (medium-chain acyl-CoA dehydrogenase) deficiency [62]. Here, ACADM is linked to hyperinsulinemic hypoglycemia, familial, 4.