The inhibitory receptor hepatitis A virus cellular receptor 2 (Havcr2) was significantly induced in AAA, while its semaphorin 4A (Sema4a)-binding competitors, leukocyte immunoglobulin-like receptor B2 (Lilrb2) and T cell immunoglobulin and mucin domain containing 4 (Timd4), were also increased. Here, HAVCR2 is linked to triple-A syndrome.