Neurofibromatosis type 2 (NF2), now more accurately referred to as NF2-related schwannomatosis (NF2-SWN)1, is a rare autosomal dominant genetic disorder with an estimated incidence of 1 in 25,000 to 40,000 live births, affecting both genders equally2-4. Here, NF2 is linked to NF2-related schwannomatosis.