It has been reported in children with hypoxic–ischemic injury or less commonly with posterior reversible encephalopathy syndrome [61], with non‐accidental head injury [62], during acute, severe manifestations of inherited monoamine neurotransmitter disorders, particularly dihydropteridine reductase deficiency [63], and encephalopathic episodes or prolonged status epilepticus in leucine‐tRNA synthetase 1 (LARS1) [64]. Here, LARS1 is linked to status epilepticus.