Type 2 VHL has been further categorized into subtypes: type 2A (associated with a lower risk of renal cell carcinoma), type 2B (associated with a higher risk of renal cell carcinoma), and type 2C (associated with isolated pheochromocytoma) (Ong et al., 2007; McNeill et al., 2009). Here, VHL is linked to hereditary pheochromocytoma-paraganglioma.