Despite the clear evidence that nerve sheath tumours in NF2-SWN were ‘schwannomas’ rather than ‘neurofibromas’ with many previous reports of neurofibromas being reclassified on pathology review [9], the name neurofibromatosis for NF2-SWN still remained in consensus statements [17, 18]. This evidence concerns the gene NF2 and plexiform neurofibroma.