Despite many reports that emphasised the lack of cutaneous manifestations in NF2-SWN patients with bilateral VS and particularly the paucity of skin tumours and café- au-lait patches in patients and families with bilateral vestibular schwannomas [3, 6, 7] case series continued to conflate NF1 and NF2-SWN as a single disorder [8]. This evidence concerns the gene NF2 and skin neoplasm.