Recently, biallelic variants in the membrane integral NOTCH2-associated receptor 2 (MINAR2) gene were reported to cause autosomal recessive deafness-120 (DFNB120, OMIM#620238) in 13 patients (4 unrelated families) with nonsyndromic congenital (9 patients) or prelingual (4 patients), severe to profound SNHL, consistent with mouse and zebrafish model of MINAR2 ablation6. This evidence concerns the gene MINAR2 and sensorineural hearing loss disorder.