Barbara Rivera et al. (11) identified a pathogenic variant of DiGeorge Syndrome Critical Region Gene 8 (DGCR8) in familial FND with schwannomatosis, while Paulsson et al. (12) and Rodrigues et al. (13) demonstrated DGCR8’s involvement in follicular-patterned thyroid carcinomas. Here, DGCR8 is linked to schwannomatosis.