SMARCB1 loss of function is also reported in other sarcomas that affect children and young people, including synovial sarcoma, the epithelioid variant of the malignant peripheral nerve sheath tumour (MPNST), epithelioid sarcoma, and the paediatric subtype of chordoma, poorly differentiated chordoma [37]. The gene discussed is SMARCB1; the disease is chordoma.