The hallmark antibodies of SS, anti-Ro (SSA) and anti-La (SSB), are present in 40%–80% of cases.8 SS also presents with systemic features, such as arthritis, vasculitis, and a predisposition to low-grade lymphomas, including mucosa-associated lymphoid tissue (MALT) lymphoma, with a lifetime risk of 5%–7.5%.2 Here, CALR is linked to synovial sarcoma.