The search for additional imprinted genes on chromosome 16 to explain the phenotype of alveolar capillary dysplasia with misalignment of pulmonary veins (ACDMPV) (OMIM# 265380), with deletions almost exclusively on the maternally inherited chromosome 16, showed evidence for novel candidate-imprinted loci on chromosome 16, namely, the maternally methylated DMR of PRR25, which is thought to be paternally expressed in supporting lymphoblastoid cells, and the paternally methylated DMR on 16q24.1 adjacent to LINC01082 mapping to the FOXF1 enhancer [40]. Here, FOXF1 is linked to alveolar capillary dysplasia with misalignment of pulmonary veins.