SLC25A13 and hyperinsulinemic hypoglycemia, familial, 4: Genetic defects of citrin (SLC25A13), a mitochondrial aspartate/glutamate transporter-2 that is associated with an aversion to carbohydrate-rich foods and fatty liver, causes elevated urinary excretion of glycerol and Gro3P in affected patients and in a mouse model of citrin deficiency (160, 308).