Analogous to what occurred in this present tumor, however, a case of WDFA of the lung with coexistence of CTNNB1 and DICER1 mutations in a 16-year-old girl with a history of TFND, ovarian Sertoli-Leydig cell tumor, and familial DICER1 syndrome has been described [41]. Here, DICER1 is linked to DICER1-related tumor predisposition.