A 40-year-old female with MEN2A had previously undergone total thyroidectomy for medullary thyroid cancer (MTC) in 1995, total left adrenalectomy for pheochromocytoma in 2007 and cortical-sparing right adrenalectomy for pheochromocytoma in 2020. This evidence concerns the gene RET and hereditary pheochromocytoma-paraganglioma.