Human ADA2 deficiency (DADA2) is an inborn error of immunity (IEI) caused by biallelic deleterious mutations in adenosine deaminase 2 (autoADA2), characterized by autoinflammation in the form of recurrent fevers and vasculitis ranging from livedo racemosa to lacunar strokes (Zhou et al., 2014; Navon Elkan et al., 2014). This evidence concerns the gene ADA2 and vasculitis.