In multivariable Cox analysis including only the variables with significant HRs in univariable analysis, serum albumin (HR 0.514, 95% CI 0.285, 0.928) and FFS + eVDI (HR 1.355, 95% CI 1.128, 1.628) at AAV diagnosis were significantly and independently associated with all-cause mortality during follow-up in patients with AAV. Here, ALB is linked to anti-neutrophil cytoplasmic antibody-associated vasculitis.