TIM8A/DDP1 (Deafness Dystonia Peptide), encoded by the TIMM8A gene, is an intermembrane space mitochondrial microprotein associated to a rare disease called Mohr‐Tranebjaerg syndrome (MTS), also known as deafness‐dystonia‐optic neuronopathy (DDON) [79]. Here, TIMM8A is linked to deafness.