We present a patient who underwent a lung transplant for FLNA deficiency and later developed posttransplant abdominal pain.<h4>Case presentation</h4>An 11-year-old female who had previously undergone a bilateral lung transplant due to FLNA deficiency, causing progressive lung disease, presented with abdominal pain and diarrhea. Here, FLNA is linked to hyperinsulinemic hypoglycemia, familial, 4.