Advances in genetic testing have identified mutations in genes such as MYH3, TPM2, TNNI2, ECEL1, TNNT3, and PIEZO2 in DAS development, with MYH3 emerging as the primary causative gene.[1] Contractures, pterygia, and spondylocarpotarsal fusion syndrome 1 (CPSFS 1), a subtype of DAS, is predominantly caused by heterozygous mutations in the MYH3 gene, including single or double allelic variants.[2]. Here, MYH3 is linked to childhood apraxia of speech.