TDP-43 has been found to co-occur with AGD in the form of small, dense, rounded neuronal cytoplasmic inclusions (NCIs) with few short dystrophic neurites (DNs), primarily observed in limbic regions, superior temporal gyrus, striatum, and midbrain, with the absence of neuronal intranuclear inclusions [82]. Here, TARDBP is linked to argyrophilic grain disease.