Mutations in the USH2A gene can disrupt these processes, leading to hearing loss and progressive vision impairment.4 Usher syndrome, particularly type 2A, presents with moderate congenital sensorineural hearing impairment and a gradual onset of retinitis pigmentosa, distinguishing it from that of type 1, which features early-onset RP and severe hearing impairment.6 Hearing loss is generally identified in childhood; however, RP occurs most often during the second decade of life, leading to delay in the diagnosis of USH.7 Since our patient was only ten years old, there was absence of RP. The gene discussed is USH2A; the disease is Usher syndrome.