USH2A and hearing loss disorder: Mutations in the USH2A gene can disrupt these processes, leading to hearing loss and progressive vision impairment.4 Usher syndrome, particularly type 2A, presents with moderate congenital sensorineural hearing impairment and a gradual onset of retinitis pigmentosa, distinguishing it from that of type 1, which features early-onset RP and severe hearing impairment.6 Hearing loss is generally identified in childhood; however, RP occurs most often during the second decade of life, leading to delay in the diagnosis of USH.7 Since our patient was only ten years old, there was absence of RP.