In another cohort of 62 patients with AAV-ILD (89% MPO-ANCA-positive), the 1-, 3-, and 5-year survival rates in the MPA-ILD group were lower than those in the non-ILD group, especially in patients with UIP, aged > 65 years, or with DAH at baseline [54]. The gene discussed is MPO; the disease is microscopic polyangiitis.