PLEC and Menkes disease: Incubation with CQ for 3 h increased MFIs to comparable levels in EBS‐MD and control fibroblasts, which is a significantly lower proportional change in MFIs in EBS‐MD fibroblasts compared with control cells, confirming that plectin deficiency coincides with impaired autophagic turnover, not only in myoblasts, but also in other cell types.