Pseudomyxoma peritonei (PMP) is a rare clinical syndrome characterized by the accumulation of mucinous ascites within the peritoneal cavity and the peritoneal implantation of mucin-producing tumor cells. This pathology was first described by Carl F. Rokitansky in 1842 [1]. Later, in 1884, Werth classified PMP as mucinous tumors associated with the ovaries [2], whereas Frankel, in 1901, proposed an alternative origin from a ruptured appendiceal mucocele [3]. This evidence concerns the gene MUC5AC and neoplasm.