CAD and maple syrup urine disease: The control group included ten patients transplanted with inborn errors of metabolism including maple syrup urine disease (MSUD), ornithine carbamoyl transferase (OTC) deficiency, carbamoyl phosphate synthetase (CPS) 1 deficiency, citrullinemia type 1, argininosuccinic aciduria, glycogenosis type 1A and type 1B or factor V deficiency (Table 1), all of whom showed no histological signs of inflammation and cirrhosis in the pathology reports.