Schwannoma development is often associated with an autosomal dominant, heritable genetic condition called NF2-related schwannomatosis (NF2-SWN, formerly known as neurofibromatosis type 2) [7], which is caused by pathogenic variants in the NF2 tumor suppressor gene, which encodes Merlin, a cytoskeletal adaptor protein with diverse biochemical functions [8]. Here, NF2 is linked to NF2-related schwannomatosis.