This constellation of clinical symptoms and neuropathologic findings is reminiscent of a recently described clinicopathologic subtype of CBD, characterized by PSP-like clinical presentations, severe tau pathology in the olivopontocerebellar system, brainstem TDP-43 pathology, and low frequency of the MAPT H1 haplotype.26 Here, TARDBP is linked to supranuclear palsy, progressive, 1.