FINCA patients often develop pulmonary fibrosis (Badura-Stronka et al., 2022; Rapp et al., 2021; Sczakiel et al., 2023; Tallgren et al., 2023; Uusimaa et al., 2018) and increased NHLRC2 expression has been shown to associate with idiopathic pulmonary fibrosis (Kreus et al., 2022). Here, NHLRC2 is linked to pulmonary fibrosis.