This need is highlighted by recent breakthroughs in the development of gene therapy for patients with otoferlin gene (OTOF) mutations, which depends on the presence of remaining cochlear sensory cells that can be repaired to restore hearing.[25] Conventional diagnostic modalities for SNHL during formal audiological testing inform clinicians as to the severity and general type of the hearing deficit,[26] but provide no cellular‐level information about the health, function, or remaining density of cochlear sensorineural cells. Here, OTOF is linked to sensorineural hearing loss disorder.