ACADM and hyperinsulinemic hypoglycemia, familial, 4: Hexanedioic acid has mainly been implicated in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency, malonyl-CoA decarboxylase deficiency, carnitine–acylcarnitine translocase deficiency, and medium-chain acyl-CoA dehydrogenase [50,51].