CPS1 and short chain acyl-CoA dehydrogenase deficiency: In the category of SCs, the most common disorder was short-chain acyl-CoA dehydrogenase deficiency (SCADD) (17/209, 8.1%, 1:20,206), followed by 3-methylcrotonyl-CoA carboxylase deficiency (3MCC) (4/209, 1.9%, 1:85,877), isobutyrylglycinuria (IBG) (3/209, 1.4%, 1:114,502) due to a deficiency of carbamoyl phosphate synthetase I (CPS) (1/209, 0.5%, 1:343,507), and type III tyrosinemia (TYR III) (1/209, 0.5%, 1:343,507).