An adult female patient with focal-onset temporal lobe epilepsy and paroxysmal kinesigenic dyskinesias/dystonia (PKD) who carried the same pathogenic PRRT2 variant as our case, c.604_607del (p.Ser202fs), was recently reported.18 This patient also had no history of SeLIE and responded to LTG.18 However, it is unclear whether the rare frameshift variant found in both patients predisposed to development of later-onset FE. Here, PRRT2 is linked to Dystonia.