DNAJC5 and glycogen storage disease VI: The models share key pathological features previously described in postmortem brain samples of human Kufs disease/CLN4 patients, such as the excessive formation of oligomers and the existence of electron dense structures detectable with electron microscopy (6, 8, 27, 29, 31, 61), which, especially in mice, mirror the autofluorescence and the GRODs found in humans.