We and others found that mis-trafficking of STING to the Golgi is the main cause of the inflammation in COPA syndrome (Deng et al., 2020; Kato et al., 2021; Lepelley et al., 2020; Mukai et al., 2021; Steiner et al., 2022). Here, STING1 is linked to autoimmune interstitial lung disease-arthritis syndrome.