MYH14 and progressive familial intrahepatic cholestasis: This was a retrospective analysis of five children with a diagnosis of PFIC associated with myosin 5B deficiency and pruritus refractory to treatment with rifampicin and ursodeoxycholic acid, starting odevixibat treatment (37.2–120 μg/kg.day) between 15 months and 10 years of age.