MODY is mainly inherited in an autosomal dominant pattern and results from variants found in one of several genes including HNF1A, GCK, HNF4A, HNF1B, PDX1, NEUROD1, KLF11, CEL, PAX4, INS, BLK, ABCC8, KCNJ11, APPL1. This disease is heterogeneous and one of its most common forms is caused by variants in the GCK gene, leading to a clinical condition known as GCK-MODY (3–6). Here, GCK is linked to MODY.